GlycosylTransferase Family 64

Activities in FamilyGlucuronyl-galactosyl-proteoglycan 4-α-N-acetylglucosaminyltransferase (EC 2.4.1.223);
Glucuronosyl-N-acetylglucosaminyl-proteoglycan α-1,4-N-acetylglucosaminyltransferase (EC 2.4.1.224);
Mechanism Retaining
3D Structure StatusGT-A
NoteThe long animal heparan synthases are made of two domains. The N-terminal domain, which adds b-1,4-GlcA residues, belongs to family GT47 while the C-terminal domain, which adds a-1,4-GlcNAc residues, belongs to family GT64. The plant homologs have a single domain.
External resourcesGlymap;
Statistics GenBank accession (757); Uniprot accession (31); PDB accession (20); 3D entries (4); cryst (0)
Eukaryota
Protein Name EC#ReferenceOrganismGenBank UniprotPDB/3D
 β-glucuronyltransferase / α-N-acetylglucosaminyltransferase (exostosin-2) (Ext2) 2.4.1.224   Bos taurus AAC35386.1
AAI26571.1
NP_803462.1
A0JN91
O77783
 
 β-glucuronyltransferase / α-N-acetylglucosaminyltransferase (Ext1) 2.4.1.224   Cricetulus griseus AAF71276.1 Q9JK82  
 heparan sulfate α-1,4-N-acetylglucosaminyltransferase-I/II (CG15110;Dext3;botv) 2.4.1.224   Drosophila melanogaster AAD34749.1
AAF57601.1
BAB89399.1
NP_523790.1
Q9XZ08  
 UDP-GlcUA:β-glucuronyltransferase / UDP-GlcNAc: α-N-acetylglucosaminyltransferase (exostosin-2;Ext2) 2.4.1.224   Homo sapiens AAB07008.1
AAB62718.1
AAC50764.1
AAC51219.1
AAH10058.1
AAH68545.1
NP_000392.1
B2R5Z6
Q6NUL1
Q93063
7SCH[B]
7SCJ[B]
7SCK[B]
7UQX[B]
7UQY[B]
7ZAY[B]
 UDP-GlcUA:β-glucuronyltransferase / UDP-GlcNAc: α-N-acetylglucosaminyltransferase (exostosin-1;Ext1) 2.4.1.224   Homo sapiens AAB62283.1
AAH01174.1
ACS08204.1
AGV77097.1
AHB20150.1
BAG35949.1
NP_000118.1
B2R7V2
Q16394
7SCH[A]
7SCJ[A]
7SCK[A]
7UQX[A]
7UQY[A]
7ZAY[A]
 exostosin-like 3 (Extl3;Extr1) 2.4.1.223   Homo sapiens AAC39598.1
AAB67602.1
AAD01877.1
AAD42041.1
AAH06363.1
AAP36017.1
AAW12588.1
AAW12594.1
ACW32787.1
ADO22448.1
BAA24080.1
BAA25445.2
BAA25445.3
BAG57702.1
NP_001431.1
A0A384NPY9
D3DST8
O43909
Q53XT3
7AU2[A,B]
7AUA[A,B]
8OG1[A]
8OG4[A,B]
 exostosin-like 1 (Extl1) 2.4.1.224   Homo sapiens AAC51141.1
AAD02840.1
AAF73172.1
AAH65528.1
AAW12597.1
CAI17130.1
NP_004446.1
Q92935  
 UDP-GlcNAc: α-1,4-N-acetylglucosaminyltransferase (Exotosin-like 2) (Extl2;EXTL2;Extr2) 2.4.1.223   Homo sapiens AAC02898.1
AAH14910.1
AAH36015.1
AAH45681.1
AAR61360.1
AAW12598.1
BAA24081.1
BAC04893.1
BAG60404.1
NP_001430.1
B2R795
B4DNZ2
D3DT60
Q05DH5
Q49A43
Q8IYF4
Q8N8F1
Q9UBQ6
 
 α-1,4-N-acetylglucosaminyltransferase-I/II / exostosin-like 3 (Extl3) 2.4.1.224   Mus musculus AAD42040.1
AAH65073.1
AAW12587.1
BAE23506.1
NP_061258.2
Q3UUW7
Q6P1H4
Q9WVL6
 
 UDP-GlcNAc: α-1,4-N-acetylglucosaminyltransferase (Extl2) 2.4.1.223   Mus musculus AAG17542.1
AAH31438.1
AAH94444.1
BAB31683.2
BAC26062.1
BAC27649.1
BAE34959.1
BAE36615.1
BAM48568.1
BAM48569.1
NP_067363.1
K0J1C6
Q3TSR0
Q3TXF7
Q8C089
Q8C197
Q9ES89
1OMX[A,B]
1OMZ[A,B]
1ON6[A,B]
1ON8[A,B]
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